{"id":115753,"date":"2025-03-14T11:41:04","date_gmt":"2025-03-14T11:41:04","guid":{"rendered":"https:\/\/www.netfarma.pt\/?p=115753"},"modified":"2025-03-14T11:41:04","modified_gmt":"2025-03-14T11:41:04","slug":"doenca-de-pompe-medicamentos-autorizados-para-uso-em-meio-hospitalar","status":"publish","type":"post","link":"https:\/\/www.netfarma.pt\/doenca-de-pompe-medicamentos-autorizados-para-uso-em-meio-hospitalar\/","title":{"rendered":"Doen\u00e7a de Pompe: Medicamentos autorizados para uso em meio hospitalar"},"content":{"rendered":"<p><strong>O Pombiliti (Cipaglucosidase) e Opfolda (Miglustato) obtiveram autoriza\u00e7\u00e3o, em termos de financiamento p\u00fablico, para serem utilizados em meio hospitalar<\/strong>, informa, hoje, no seu portal a Autoridade Nacional do Medicamento e Produtos de Sa\u00fade (Infarmed).<\/p>\n<p>Os medicamentos est\u00e3o agora autorizados na indica\u00e7\u00e3o: “<strong>Pombiliti (cipaglucosidase alfa) \u00e9 uma terap\u00eautica de substitui\u00e7\u00e3o enzim\u00e1tica a longo prazo utilizada em combina\u00e7\u00e3o com o estabilizador de enzimas miglustato para o tratamento de adultos com doen\u00e7a de Pompe de in\u00edcio tardio (defici\u00eancia de \u03b1-glucosidase \u00e1cida [GAA])”<\/strong>.<\/p>\n<p>O relat\u00f3rio p\u00fablico desta avalia\u00e7\u00e3o est\u00e1 dispon\u00edvel na Infomed.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>O Pombiliti (Cipaglucosidase) e Opfolda (Miglustato) obtiveram autoriza\u00e7\u00e3o, em termos de financiamento p\u00fablico, para serem utilizados em meio hospitalar, informa, … <\/p>\n","protected":false},"author":29,"featured_media":38895,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"episode_type":"audio","audio_file":"","cover_image":"","cover_image_id":"","duration":"","filesize":"","date_recorded":"","explicit":"","block":"","itunes_episode_number":"","itunes_title":"","itunes_season_number":"","itunes_episode_type":"","filesize_raw":"","footnotes":""},"categories":[108,110,64,70],"tags":[14946,12087,11379,125,14948,14947,14945],"series":[],"class_list":["post-115753","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-farmacia","category-industria","category-noticias","category-recentes","tag-cipaglucosidase","tag-doenca-de-pompe","tag-financiamento-de-medicamentos","tag-infarmed","tag-miglustato","tag-opfolda","tag-pombiliti"],"episode_featured_image":"https:\/\/www.netfarma.pt\/wp-content\/uploads\/infarmed-3.png","episode_player_image":"https:\/\/www.netfarma.pt\/wp-content\/plugins\/seriously-simple-podcasting\/assets\/images\/no-album-art.png","download_link":"","player_link":"","audio_player":false,"episode_data":{"playerMode":"dark","subscribeUrls":[],"rssFeedUrl":"https:\/\/www.netfarma.pt\/feed\/podcast\/netfarma","embedCode":"<blockquote class=\"wp-embedded-content\" data-secret=\"34NHpzq9vV\"><a href=\"https:\/\/www.netfarma.pt\/doenca-de-pompe-medicamentos-autorizados-para-uso-em-meio-hospitalar\/\">Doen\u00e7a de Pompe: Medicamentos autorizados para uso em meio hospitalar<\/a><\/blockquote><iframe sandbox=\"allow-scripts\" security=\"restricted\" src=\"https:\/\/www.netfarma.pt\/doenca-de-pompe-medicamentos-autorizados-para-uso-em-meio-hospitalar\/embed\/#?secret=34NHpzq9vV\" width=\"500\" height=\"350\" title=\"“Doen\u00e7a de Pompe: Medicamentos autorizados para uso em meio hospitalar” — Netfarma\" data-secret=\"34NHpzq9vV\" frameborder=\"0\" marginwidth=\"0\" marginheight=\"0\" scrolling=\"no\" class=\"wp-embedded-content\"><\/iframe><script type=\"text\/javascript\">\n\/* <![CDATA[ *\/\n\/*! This file is auto-generated *\/\n!function(d,l){\"use strict\";l.querySelector&&d.addEventListener&&\"undefined\"!=typeof URL&&(d.wp=d.wp||{},d.wp.receiveEmbedMessage||(d.wp.receiveEmbedMessage=function(e){var t=e.data;if((t||t.secret||t.message||t.value)&&!\/[^a-zA-Z0-9]\/.test(t.secret)){for(var s,r,n,a=l.querySelectorAll('iframe[data-secret=\"'+t.secret+'\"]'),o=l.querySelectorAll('blockquote[data-secret=\"'+t.secret+'\"]'),c=new RegExp(\"^https?:$\",\"i\"),i=0;i<o.length;i++)o[i].style.display=\"none\";for(i=0;i<a.length;i++)s=a[i],e.source===s.contentWindow&&(s.removeAttribute(\"style\"),\"height\"===t.message?(1e3<(r=parseInt(t.value,10))?r=1e3:~~r<200&&(r=200),s.height=r):\"link\"===t.message&&(r=new URL(s.getAttribute(\"src\")),n=new URL(t.value),c.test(n.protocol))&&n.host===r.host&&l.activeElement===s&&(d.top.location.href=t.value))}},d.addEventListener(\"message\",d.wp.receiveEmbedMessage,!1),l.addEventListener(\"DOMContentLoaded\",function(){for(var e,t,s=l.querySelectorAll(\"iframe.wp-embedded-content\"),r=0;r<s.length;r++)(t=(e=s[r]).getAttribute(\"data-secret\"))||(t=Math.random().toString(36).substring(2,12),e.src+=\"#?secret=\"+t,e.setAttribute(\"data-secret\",t)),e.contentWindow.postMessage({message:\"ready\",secret:t},\"*\")},!1)))}(window,document);\n\/* ]]> *\/\n<\/script>\n"},"_links":{"self":[{"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/posts\/115753","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/users\/29"}],"replies":[{"embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/comments?post=115753"}],"version-history":[{"count":1,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/posts\/115753\/revisions"}],"predecessor-version":[{"id":115754,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/posts\/115753\/revisions\/115754"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/media\/38895"}],"wp:attachment":[{"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/media?parent=115753"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/categories?post=115753"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/tags?post=115753"},{"taxonomy":"series","embeddable":true,"href":"https:\/\/www.netfarma.pt\/wp-json\/wp\/v2\/series?post=115753"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}